What+is+Medium-Chain+ketoacyl-CoA+Thiolase?

Medium-Chain Ketoacyl-CoA Thiolase is a rare disorder where the body lacks enzymes needed to convert fats into energy. These fats build up in the body and cause damage.
To prevent this disorder your infant is to avoid fasting for more than 12 hours. Infants require frequent feedings, It is recommended that toddlers receive 2 g/kg of uncooked cornstarch as a source of carbohydrates at bedtime for a supplement of glucose over night.

Symptoms of MCKAT is Vomiting, Lack of energy, Low blood sugar, Seizures, Breathing difficulty, Liver problems, Cardiac arrest, Brain damage, Coma, Risk of sudden death and Neurological damage.



= Bibliography =

"Medium-chain 3-ketoacyl-coA thiolase deficiency ." //CheckOrphan//. GetReelHealth, 2006-2010. Web. 9 June 2011. .